Carnitine is an important factor for the transport of long-chain fatty acids bound to carnitine (carnitine acyltransferase) into the mitochondrial matrix for subsequent β-oxidation. There are two enantiomers: D- and L-carnitine. Only the L-isomer is physiologically active.
MitoPedia topics: Substrate and metabolite
Application in HRR
- L-carnitine: Sigma Aldrich; C0158; FW=161.2